Assessment of Ataxia Rating Scales and Cerebellar Functional Tests: Critique and Recommendations

Perez-Lloret S, van de Warrenburg B, Rossi M, Rodríguez-Blázquez C, Zesiewicz T, Saute JAM, Durr A, Nishizawa M, Martinez-Martin P, Stebbins GT, Schrag A, Skorvanek M; and members of the MDS Rating Scales Review Committee; Mov Disord. 2020 Oct 6. doi: 10.1002/mds.28313

We identified some "recommended" scales and functional tests for the assessment of patients with major hereditary ataxias and other cerebellar disorders. The main limitations of these instruments include the limited assessment of patients in the more severe end of the spectrum and children. Further research in these populations is warranted.