Sunday, May 5, 2013

Bioenergetics Reprogrammed in a Cellular Model of Friedreich's Ataxia: Frataxin Deficiency Affects Formation of Respiratory Supercomplexes and Down-regulates Both OXPHOS and Glycolysis.

Bioenergetics Reprogrammed in a Cellular Model of Friedreich's Ataxia: Frataxin Deficiency Affects Formation of Respiratory Supercomplexes and Down-regulates Both OXPHOS and Glycolysis. Van Houten B, Wang T; Journal of Biomolecular Techniques : JBT [2013, 24(Suppl):S54-S55]

Keywords: Friedreich's ataxia (FRDA), glycolysis, OXPHOS, glucose metabolism, fatty acid oxidation, bioenergetics reprogramming.