Friday, September 21, 2012

Relation of Cytosolic Iron Excess to Cardiomyopathy of Friedreich's Ataxia

Relation of Cytosolic Iron Excess to Cardiomyopathy of Friedreich's Ataxia, R. Liane Ramirez, Jiang Qian, Paolo Santambrogio, Sonia Levi, Arnulf H. Koeppen. The American Journal of Cardiology, Available online 20 September 2012.

Keywords: Cardiomyopathy, Friedreich's ataxia, frataxin gene, iron (Fe)-sulfur clusters, sarcoplasmic Fe, cardiomyocyte hypertrophy, fiber necrosis, myocardial scarring, Fe, ferritin, ferroportin, zinc.