Friedreich Ataxia: An Update on Animal Models, Frataxin Function and Therapies

Advances in experimental medicine and biology,   ISSN 0065-2598  CODEN AEMBAP. 2009, vol. 652, pp. 247-261 [15 page(s) (article)

GONZALEZ-CABO Pilar ; VICENTE LLORENS José ; PALAU Francesc ; MOLTO Maria Dolores ;  

Keywords: Friedreich ataxia ; Frataxin ; Mitochondria ; Iron-sulfur clusters ; Oxidative stress ; Oxidative phosphorylation ; Antioxidant therapy ; Iron chelators ; Recombinant human erythropoietin ; Histone deacetylase inhibitors ;