Changes in mitochondrial glutathione levels and protein thiol oxidation in ∆yfh1 yeast cells and the lymphoblasts of patients with Friedreich's ataxia.

Biochim Biophys Acta. 2011 Nov 11;1822(2):212-225

Bulteau AL, Planamente S, Jornea L, Dur A, Lesuisse E, Camadro JM, Auchère F.
CRICM-INSERM-UMRS975, CNRS UMR 7225-UPMC, Hôpital de la Salpétrière, Physiopathologie cellulaire et moléculaire des maladies mitochondriales, 91, bd de l'hôpital, salle 336, 75651 Paris Cedex 13, France.

Keywords: Friedreich's ataxia (FRDA), frataxin, iron, iron-sulfur cluster, oxidative stress, glutathione homeostasis, protein thiols, GSH/GSSG ratio, aconitase, KGDH.