Thursday, December 15, 2011

HSC20 interacts with Frataxin and is involved in iron-sulfur cluster biogenesis and iron homeostasis

Hum. Mol. Genet. (2011) doi: 10.1093/hmg/ddr582

Yuxi Shan and Gino Cortopassi
Molecular Biosciences, 1120 Haring Hall, University of California, Davis, CA 95616

Keywords: Friedreich’s ataxia (FRDA), frataxin, mitochondrial iron-sulfur cluster (ISC) biosynthesis, ISC assembly machinery, mitochondrial chaperone HSC20, iron-dependent, ISCU/Nfs1, GRP75 ISC chaperone.