Thursday, November 25, 2010

Feasibility of Implantable Cardioverter Defibrillator Treatment in Five Patients With Familial Friedreich's Ataxia—A Case Series

Artificial Organs, Volume 34, Issue 11, pages 1061–1065, November 2010, DOI: 10.1111/j.1525-1594.2010.01140.x

Keywords: Friedreich's ataxia (FRA), familial cardiomyopathy, the most common cause of death, implantable cardioverter defibrillator (ICD), University Hospital of Goettingen, frataxin locus, electrocardiogram, ventricular dysfunction, ventricular tachyarrhythmias.

"Our experience implies the safe use of ICD in children with FRA"