Wednesday, November 4, 2009

Frataxin interacts with Isu1 through a conserved tryptophan in its beta-sheet.

Hum Mol Genet. 2009,  Nov 2.

Leidgens S, De Smet S, Foury F.

Unité de Biochimie Physiologique, Institut des Sciences de la Vie, Université Catholique de Louvain, Croix du Sud 5-15, 1348 Louvain-la-Neuve, Belgium.

Keywords: Friedreich's ataxia, frataxin, iron-sulfur (Fe/S) clusters, Yfh1, Isu1, beta-sheet platform, Q129A, I130A, W131A(F), R141A, low aconitase activity, Gln-129, Trp-131, Arg-141, aromatic side chain.

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