Exploring frataxin function.

IUBMB Life. 2011 Nov 17. doi: 10.1002/iub.577. [Epub ahead of print]

Busi MV, Gomez-Casati DF.

Centro de Estudios Fotosintéticos y Bioquímicos (CEFOBI-CONICET), Universidad Nacional de Rosario, Suipacha 531, 2000, Rosario, Argentina and Instituto de Investigaciones Biotecnológicas (IIB-INTECH), Universidad Nacional de General San Martín (UNSAM), Argentina.

Keywords: Frataxin, nuclear-encoded mitochondrial protein, phenotype of Friedreich's ataxia, Fe-S cluster, heme synthesis, energy conversion, oxidative phosphorylation, iron handling, oxidative damage.