Molecular and Functional Alterations in a Mouse Cardiac Model of Friedreich Ataxia : Activation of the Integrated Stress Response, eIF2α Phosphorylation, and the Induction of Downstream Targets. Michael Li-Hsuan Huang, Sutharshani Sivagurunathan, Samantha Ting, Patric J. Jansson, Christopher J.D. Austin, Matthew Kelly, Christopher Semsarian, Daohai Zhang, Des R. Richardson. The American Journal of Pathology, Available online 22 July 2013. http://dx.doi.org/10.1016/j.ajpath.2013.05.032