Friday, May 15, 2026

62 Development and Translation of PPL-001, an autologous, gene-edited CD34+ hematopoietic stem cell Therapy for Friedreich’s Ataxia

2026 Annual Meeting of the American Society of Gene and Cell Therapy: ASGCT 2026 Annual Meeting Abstracts. Available online 8 May 2026, Version of Record 8 May 2026.  62 

Development and Translation of PPL-001, an autologous, gene-edited CD34+ hematopoietic stem cell Therapy for Friedreich’s Ataxia  Anusha Sivakumar, Colin Exline, Stephanie Cherqui.

 Here, we present a GMP-compliant, commercially/clinically scalable manufacturing process and safety data of PPL-001, aimed at initiating the first-in-human HSPC and genome editing clinical trial for FRDA. 

These promising results of scale-up feasibility and safety support our efforts in clinical translation of CRISPR/Cas9 gene edited CD34+ HSPCs as a novel treatment approach for Friedreich’s ataxia.