Highly specific ubiquitin-competing molecules effectively promote frataxin accumulation and partially rescue the aconitase defect in Friedreich ataxia cells

Highly specific ubiquitin-competing molecules effectively promote frataxin accumulation and partially rescue the aconitase defect in Friedreich ataxia cells. Alessandra Rufini, Francesca Cavallo, Ivano Condo’, Silvia Fortuni, Gabriella De Martino, Ottaviano Incani, Almerinda Di Venere, Monica Benini, Damiano Sergio Massaro, Gaetano Arcuri, Dario Serio, Florence Malisan, Roberto Testi; Neurobiology of Disease, Available online 27 December 2014, ISSN 0969-9961, http://dx.doi.org/10.1016/j.nbd.2014.12.011.

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